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患者男性,14岁,因自幼右眼视力差就诊。眼部检查:右眼视力眼前指数;左眼视力0.6,不能矫正。眼压:右眼26mmHg(1mmHg=0.133kPa),左眼24mmHg。双眼结膜无明显充血,角膜水平径15mm,角膜后弹力层破裂(Haab线);前房轴深5CT,周边前房深1CT;虹膜纹理清,房水清,晶状体透明;视乳头边界清,C/D:右眼0.9,左眼0.7,视网膜平伏,黄斑中心凹光反射存在。
前房角及UBM检查:双眼前房角开放,见有较多中胚叶组织残留。裂隙灯显微镜检查:双眼角膜弧度无明显异常。相干光断层扫描(OCT)视神经纤维层厚度:双眼较正常眼变薄,右眼减少82%,左眼减少40%。视野检查:右眼全盲,左眼弓形暗点。 问题:患者可能的诊断是( )
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